6% GSI-IX (0.016 person/y; 95% confidence interval, 0.83-2.79%), and SCD 0.93% (0.0093 person/y; 95% confidence interval, 0.37-1.92%).

Conclusions-Left ventricular hypertrophy is rare in children with TNNT2 mutations. Left ventricular hypertrophy is absent in the minority of adults, but most have an abnormal ECG. Despite adverse family histories, the rate of cardiovascular death during follow-up was similar to that reported in large referral populations. (Circ Cardiovasc Genet. 2012;5:10-17.)”
“This

paper is devoted to the phenomenon of resonant transmission in three-dimensional electromagnetic band gap structures (EBGs), achieved by introducing a defect into an EBG structure with the corresponding resonance frequency of the defect lying within the initial EBG region. It is shown that the resonance frequency of an EBG air cavity (acceptor defect)

can either increase or decrease with increasing cavity dimensions. In particular, this paper demonstrates both experimentally and theoretically that the resonance frequency of a woodpile air cavity, formed by the partial removal of a woodpile bar, increases with increasing cavity size; it increases continuously or saturates depending on the field polarization with respect to the cavity orientation. The results obtained in this paper can be used for designing EBG devices based on resonant transmission.”
“Background-Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is characterized by frequent life-threatening ventricular arrhythmias, diagnosed on average in the teens to mid-50s and commonly treated by implantable cardioverter defibrillators (ICDs). As younger GW2580 chemical structure age and high frequency of ICD discharges are risk factors for difficulties in psychosocial CYT387 nmr adjustment, we developed a study to assess psychosocial adjustment among patients with ARVD/C and to determine risk factors for poor adjustment in this high-risk population.

Methods

and Results-Eighty-six adults enrolled in the Johns Hopkins ARVD Registry (38 male; mean age, 45.4 +/- 12.9 years), with an ICD in place for a median 3.2 years (range, 0.2 to 20.1 years), completed a set of questionnaires measuring ICD-specific anxiety (Florida Shock Anxiety Scale), device acceptance (Florida Patient Acceptance Survey), anxiety and depression (Hospital Anxiety and Depression Scale), and functional capacity (Duke Activity Status Index). Although overall device acceptance (Florida Patient Acceptance Survey mean, 76.7 +/- 15.3) was normative, patients with ARVD/C had substantially elevated body image concerns (Florida Patient Acceptance Survey subscale mean, 17.9 +/- 23.5) and device-related distress (subscale mean, 26.5 +/- 19.2), particularly among younger patients (P<0.01). Patients with ARVD/C had elevated ICD-specific (Florida Shock Anxiety Scale mean, 22.9 +/- 7.8) and general clinical anxiety (Hospital Anxiety and Depression Scale anxiety subscale mean, 6.2 +/- 3.9).